Congenital Heart Disease

Definition

After careful study, it is our belief that ALL complex congenital heart conditions should be coded with every patient admission/encounter. These conditions should be considered as “active” problems rather than as a patient’s resolved history. As such, they should be coded as either primary or secondary diagnoses, depending on the reason for admission. Whether or not the surgery was palliative or part of a staged surgical plan is irrelevant, and these codes should be used for these patients for a lifetime. These issues repaired or not, have real bearing on a patient’s risk because they require:

  1. Clinical Evaluation - These patients may have Cardiology notified or consulted while admitted and have regularly scheduled visits with Cardiology for many years after surgery.

  2. Therapeutic Treatment - These patients are frequently on home medications that need to be continued while inpatient for years after surgery, or even for life.

  3. Diagnostic Procedures - Additional studies such as echocardiograms, electrocardiograms (EKGs), and telemetry are frequently needed during admission.

  4. Extended Length of Hospital Stay - Patients with underlying congenital heart conditions frequently require an extended hospitalization period.

  5. Increased Nursing Care and/or Monitoring - When these patients are admitted, they often require higher level care (frequently IMC), where they receive lower nurse-to-patient ratio and continuous cardiopulmonary monitoring.

Single Ventricle Anatomy Hypoplastic Right Heart
Hypoplastic Left Heart Double Outlet Right Ventricle
Partial Anomalous Pulmonary Venous Connection (PAPVC) Total Anomalous Pulmonary Venous Connection (TAPVC)
Tetrology of Fallot Tricuspid Atresia
Atrioventricular Canal Coarctation

Less complex issues still need to be coded as “history” once repaired (unless they are currently being followed by a Cardiologist). These are atrial septal defects (ASD), ventricular septal defects (VSD), patent ductus arteriosus (PDA), and patent foramen ovale (PFO).

Note: these less complex conditions may be present along with a more complex congenital heart condition, i.e. VSD with TAPVC. Following surgical repair, in subsequent admissions, we would still capture both the codes, TAPVC and VSD.

Diagnoses

Complex congenital heart diagnoses include but are not limited to: